Vol. 36 (2021)
Cartas científicas

Primary pericardial T/NK cell lymphoma. Case report

Guillermo Agorrody
Instituto Nacional de Cirugía Cardíaca (INCC). Montevideo, Uruguay / Departamento de Cardiología, Servicio Médico Integral (SMI). Montevideo, Uruguay.
Amparo Fernández
Instituto Nacional de Cirugía Cardíaca (INCC). Montevideo, Uruguay / Departamento de Cardiología, Servicio Médico Integral (SMI). Montevideo, Uruguay.
Facundo Ríos
Instituto Nacional de Cirugía Cardíaca (INCC). Montevideo, Uruguay / Departamento de Cardiología, Servicio Médico Integral (SMI). Montevideo, Uruguay.
María José Arocena
Instituto Nacional de Cirugía Cardíaca (INCC). Montevideo, Uruguay / Departamento de Cardiología, Servicio Médico Integral (SMI). Montevideo, Uruguay.
Lilián Díaz
Departamento de Hematología, Servicio Médico Integral (SMI). Montevideo, Uruguay.
Jorge Estigarribia
Instituto Nacional de Cirugía Cardíaca (INCC). Montevideo, Uruguay.
Published 01-04-2021

Keywords:

Cardiac tumors, Pericardial tumors, Pericardial effusion, Pericardial tamponade

Abstract

Primary cardiac lymphomas are a rare subtype of lymphomas in which the primary lesion is in the heart. The tumors are usually located in the right atria, followed by the pericardium and are frequently infiltrative. Mortality is remarkably high in this group and the delayed diagnosis is the main factor for its poor prognosis. We describe the case of a patient that presented with obstructive shock due to profuse pericardial effuse caused by a rare kind of primary cardiac tumor, a T/NK cell pericardial lymphoma.