Vol. 34 No. 2 (2019): Revista Uruguaya de Cardiología
Cartas científicas

Anomalous origin of the left coronary artery from the pulmonary artery, ALCAPA syndrome. First case report in Uruguay

  • Juan Pablo Bachini,
  • Alejandra Amodio,
  • Rodrigo Guzmán,
  • Nicolás Fernández,
  • Ivanna Duro,
  • Sergio Viñas,
  • Médica Uruguaya Instituto de Cardiología Integral. Montevideo, Uruguay,
Published 21-11-2019

Keywords:

PULMONARY ARTERY, HEART DEFECTS, CONGENITAL, ALCAPA SYNDROME

Abstract

The anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA syndrome) is a rare entity with a high infant mortality rate during first year of life reaching up to 90%. This fact makes this condition extremely uncommon among adults. We report for the first time in our country an adult presentation in a 32-year-old woman. This patient presented with a history of exertional angina and a transthoracic echocardiogram showed suggestive clues for the diagnosis of ALCAPA, then confirmed with coronary angiography. The patient underwent successfull surgical correction with Takeuchi technique.

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